Vertical Talus
Editors: Frassica, Frank J.; Sponseller, Paul D.; Wilckens, John H.
Title: 5-Minute Orthopaedic Consult, 2nd Edition
Copyright ©2007 Lippincott Williams & Wilkins
> Table of Contents > Vertical Talus
Vertical Talus
Paul D. Sponseller MD
Basics
Description
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Congenital vertical talus is an uncommon disorder, a rigid flatfoot that requires early identification and treatment.
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Its essence is a dislocation of the talonavicular joint with associated adaptive changes.
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It may be unilateral or bilateral.
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>1/2 of affected patients have other neurologic, genetic, or connective tissue disorders.
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The deformity occurs in utero, but it may be 1st identified any time from infancy to adulthood.
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Classification:
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Isolated
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Syndrome-related
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Synonyms: Congenital convex pes planus; Congenital rigid rocker-bottom foot
Epidemiology
Incidence
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Rare, but a high association with other disorders and anomalies:
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10% of children with myelodysplasia have congenital vertical talus (1).
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It also can be associated with trisomy 13, 15, and 18 and with arthrogryposis or Larsen syndrome.
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In 20–40% of cases, congenital vertical talus occurs as an isolated anomaly (1,2).
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It affects males and females equally.
Risk Factors
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Myelodysplasia
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Ligamentous laxity
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Arthrogryposis multiplex
Genetics
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Unknown, but probably variable
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In some cases, vertical transmission as an autosomal dominant trait with incomplete penetrance has been described.
Etiology
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Muscle imbalance between the dorsiflexor
muscles of the forefoot and plantarflexor muscles of the hindfoot cause
disruption in the middle of the foot (talonavicular joint). -
Ligamentous laxity and in utero malposition may be causative factors in some cases.
Associated Conditions
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Arthrogryposis
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Larsen syndrome
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Myelomeningocele
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Trisomy 13, 15, 18
Diagnosis
Signs and Symptoms
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Signs: Moderate reversal of the arch and a crease on the dorsum of the foot near the sinus torsi
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Symptoms: Lack of push-off strength, painful callus under the head of the talus possible if untreated by walking age
Physical Exam
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Check the other extremities, as well as the spine, for anomalies.
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Measure strength in both lower extremities.
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Observe the foot in stance and gait if the child is walking.
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It is easily distinguishable from the more common calcaneovalgus and flexible flatfoot.
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The sole of the foot is convex, has a rocker bottom, and is rigid.
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The heel is in a fixed equinus with a tight Achilles tendon.
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The head of the talus is prominent and palpable medially in the sole of the foot.
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The hindfoot is in valgus.
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The forefoot is abducted and in dorsiflexion at the midtarsal joint (Fig. 1).
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As the patient becomes older, the appearance of the foot becomes more distinctive.Fig. 1. Vertical talus produces a dorsal crease and a plantar prominence.
Tests
Imaging
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Obtain radiographs.
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The talus is plantarflexed (on lateral films) and angled medially (on AP films).
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The navicular is dislocated dorsally and is perched on the neck of the talus.
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The forefoot is displaced dorsally and abducted.
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The calcaneus is in a fixed equinus.
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Only the most posterior aspect of the
talus articulates with the tibia and, in extreme cases, the talus is
parallel to the tibia. -
The diagnosis is confirmed in extreme
plantarflexed views, when the navicular will not reduce, and the line
through the talar axis passes plantar to the metatarsal axis.-
Normal is dorsal to the cuboid and in line with the metatarsal axis.
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However, the navicular does not ossify until ~3 years of age, in the normal foot or the foot with congenital vertical talus.
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The position of the navicular may be inferred from the orientation of the first metatarsal.
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Pathological Findings
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The calcaneus is in equinus and laterally displaced.
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The talus is hypoplastic, angled medially, and plantarflexed.
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Fixed dorsal dislocation of the navicular is noted.
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Contracture of the Achilles tendon (posteriorly) is evident.
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Contracture of the toe extensor and the tibialis anterior (anteriorly) is seen.
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Specially positioned plantar flexion lateral radiograph is helpful (see later).
Differential Diagnosis
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Calcaneovalgus foot
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Flexible flatfoot
P.481
Treatment
General Measures
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Stretching
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Surgery
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If the condition is recognized, surgical intervention is preferred before the patient is 2 years old.
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Casting and manipulation alone usually are not effective, although they should be used preoperatively to stretch soft tissue.
Activity
Unrestricted
Surgery
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The essential features are reduction (open or closed) and pinning of the talonavicular joint.
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Although open surgery previously was the norm (1,3), reduction and percutaneous pin fixation with an Achilles tenotomy recently has become an accepted technique (4).
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The associated contracted tendons (Achilles and, if needed, anterior tibialis) also should be lengthened.
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The medial joint capsules may be stabilized, or, in children ≥3 years old, the talonavicular joint may be fused.
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Children >5 years old may require triple arthrodesis.
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Postoperative percutaneous PINS of the talonavicular joint usually are removed at 6 weeks.
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Postoperative bracing often is used for a number of months.
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Late treatment requires subtalar fusion.
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Recurrent deformity is treated with soft-tissue reconstruction and subtalar fusion.
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In adolescents and adults, salvage is
performed by triple arthrodesis and often requires removal of a large
portion of the talus.
Follow-up
Patients should be followed throughout childhood to monitor the growth of the foot.
Prognosis
If untreated, the condition produces progressive disability.
Complications
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Complications of nontreatment: Callus, skin breakdown, poor push-off
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Complications of treatment: Stiffness, residual varus or valgus, need for additional surgery
Patient Monitoring
Even after surgery, the patient should be followed periodically to verify normal growth.
References
1. Morrissy
RT, Giavedoni BJ, Coulter-O’Berry C. The child with a limb deficiency.
In: Morrissy RT, Weinstein SL, eds. Lovell and Winter’s Pediatric
Orthopaedics, 6th ed. Philadelphia: Lippincott Williams & Wilkins,
2006:1329–1381.
RT, Giavedoni BJ, Coulter-O’Berry C. The child with a limb deficiency.
In: Morrissy RT, Weinstein SL, eds. Lovell and Winter’s Pediatric
Orthopaedics, 6th ed. Philadelphia: Lippincott Williams & Wilkins,
2006:1329–1381.
2. Ogata K, Schoenecker PL, Sheridan J. Congenital vertical talus and its familial occurrence: An analysis of 36 patients. Clin Orthop Relat Res 1979;139:128–132.
3. Seimon LP. Surgical correction of congenital vertical talus under the age of 2 years. J Pediatr Orthop 1987;7:405–411.
4. Dobbs MB, Purcell DB, Nunley R, et al. Early results of a new method of treatment for idiopathic congenital vertical talus. J Bone Joint Surg 2006;88A:1192–1200.
Miscellaneous
Codes
ICD9-CM
754.69 Congenital vertical talus
Patient Teaching
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Patients should be informed of the chances of inheritance in future children.
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The natural history of this condition, if
left untreated, which is severe callus formation, skin breakdown, and
poor push-off, also should be discussed. -
The risk of hip dysplasia should be mentioned and excluded.
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The possible need for additional surgery should be mentioned.
FAQ
Q: How is vertical talus commonly recognized?
A: By the deep crease in the sinus tarsi and the plantar convexity.
Q: Does it resolve spontaneously?
A: No, it does not.